HCU Express Plus Oral Supplement is a powdered methionine-free formula used to treat Homocystinuria (HCU). It contains a combination of essential and non-essential amino acids, carbohydrates, docosahexaenoic acid (DHA), vitamins, and minerals, as well as an updated nutrition profile in accordance with recommendations to ensure appropriate consumption of nutrients lacking in a typical low-protein diet.

Features:

• Unflvored
• Available in 15 g and 20 g protein equivalent packets
• Convenient, pre-measured packaging: no weighing or measuring required, and easily portable
• Mix one packet with 3 fl oz of water or allowed beverage to make a low-volume drink
• Each can be blended as is or readily customized with permitted beverages to provide a variety of flavors

Dosage and Administration: To be determined by the clinician or dietitian and is dependent on the age, body weight, and medical condition of the patient.

• Each 25 g packet of HCU express plus15 provides 15 g of protein equivalent.
• Each 34 g packet of HCU express plus20 provides 20 g of protein equivalent.

Preparation Guidelines:

• Empty the contents of the packet into a cup with a lid.2
• Add 90 ml (3 fl oz) of cold water or other permitted beverage
• Secure the lid and shake well for 10 seconds until the powder dissolves

The product should be prepared fresh and consumed right away. If this is not possible, any prepared product must be properly wrapped and consumed within 4 hours at room temperature or within 24 hours if refrigerated. Shake again before using. Following product consumption, water or allowed liquids should be consumed.

Storage: Store in a cool dry place. Packets are designed for single use and should be used immediately once opened. Any unused powder in a packet must be tightly sealed and used within 24 hours.

Important Notice:

• For enteral use only.
• Not for intravenous use.
• Not for use as a sole source of nutrition.
• Must only be consumed by people with proven HCU under strict medical supervision.
• Diet must be supplemented with natural protein, water, and other nutrients in prescribed quantities to supply methionine, fluid, and general nutrition requirements.