Ketonex-1 Unflavored Amino Acid-Modified Infant Formula is a specialized nutritional solution formulated to support infants and toddlers with maple syrup urine disease (MSUD) or beta-keto thiolase deficiency. This formula delivers targeted nutrition for metabolic management by providing essential nutrients while excluding specific amino acids that cannot be tolerated. Use under medical supervision.

Features

• Halal, Non-GMO, Gluten-free, and Lactose-free formulation.
• Developed with a nutrient profile tailored for infants and toddlers.
• Provides 6.6% of energy from linoleic acid for essential fatty acid support.
• Includes DHA and ARA to help support early brain and eye development.
• Branched-chain amino acid–free to allow greater intake of intact protein as prescribed.
• Approximately 40% of energy from fat helps maintain appropriate formula osmolality.
• When used according to Abbott Nutrition Support Protocols, it provides complete and balanced nutrient intake.
• L-carnitine (100 mg/100 g) and taurine (40 mg/100 g) help supply levels similar to those naturally present in human milk and animal-derived foods.

Ingredients: Corn Syrup Solids, High Oleic Safflower Oil, Coconut Oil, Soy Oil, L-Alanine, Modified Corn Starch, L-Proline. Less than 2% of L-Lysine, L-Arginine, Calcium Phosphate, L-Glutamine, Potassium Phosphate, Glycine, L-Tyrosine, L-Phenylalanine, L-Serine, L-Asparagine, L-Threonine, Sodium Citrate, Potassium Citrate, Magnesium Chloride, L-Histidine, M. Alpina Oil, L-Methionine, C. Cohnii Oil, Calcium Carbonate, Citric Acid, L-Glutamic Acid, Ascorbic Acid, L-Cystine Dihydrochloride, Inositol, L-Tryptophan, Choline Chloride, L-Aspartic Acid, L-Carnitine, Taurine, Ferrous Sulfate, Ascorbyl Palmitate, Zinc Sulfate, dl-Alpha-Tocopheryl Acetate, Mixed Tocopherols, Calcium Pantothenate, Niacinamide, Manganese Sulfate, Thiamine Hydrochloride, Copper Sulfate, Vitamin A Palmitate, Riboflavin, Pyridoxine Hydrochloride, Potassium Iodide, Folic Acid, Phylloquinone, Chromium Chloride, Sodium Selenate, Sodium Molybdate, Biotin, Vitamin D3, Vitamin B12, and Salt.

Instructions for Use: Use Only As Directed by a Physician

Your baby's health depends on carefully following these directions. Proper hygiene, handling, and storage are important when preparing infant formula. Failure to follow these directions could result in severe harm. Ask your baby's doctor if you need to use cooled, boiled water for mixing and if you need to boil (sterilize) bottles, nipples, and rings before use.

• Wash your hands, surfaces, and utensils.
• Pour the prescribed amount of water into a clean container.
• Add the prescribed amount of Ketonex-1 powder (and other ingredients if recommended).
• Shake well for 10-15 seconds; if using a blender, mix no more than 5 seconds.
• Pour mixture into clean feeding bottles or containers; cap.
• Once feeding begins, use within 1 hour or discard.

Approximate weights for unpacked, level U.S. standard dry household measures for powder*

* For the most accurate results, Ketonex-1 should be weighed on a scale that reads in grams.

Storage and Handling

• Once mixed, store bottles or containers in the refrigerator and feed to the baby or child within 24 hours
• Store unopened or opened cans at room temperature; avoid extreme temperatures.
• Use opened can content within 1 month.

Precaution

• Not for IV use.
• Not intended as a sole source of nutrition.
• Do not boil the mixture or use terminal sterilization.
• Never use a microwave oven to warm the formula. Serious burns can result.
• Give only to infants and toddlers with proven maple syrup urine disease who are under medical supervision.
• Must be supplemented with protein and fluid in prescribed amounts to completely meet isoleucine, leucine, valine, and water requirements.
• Powdered infant formulas are not sterile and should not be fed to premature infants or infants who might have immune problems unless directed and supervised by your baby's doctor.